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Bay Biosciences provides high quality Rhabdomyosarcoma tumor tissue samples FFPE blocks from unique pediatric patients for research, development and discovery. Detailed clinical data and pathology annotations including patient’s corresponding diagnostic test values associated with the Rhabdomyosarcoma tumor tissue samples are provided to a valued pharmaceutical customer for In-vitro research and drug discovery.

Rhabdomyosarcoma (RMS) Tumors Overview

Rhabdomyosarcoma (RMS) is a rare type of highly aggressive cancerous tumor that forms in soft tissue such as muscles, specifically skeletal (voluntary) muscle tissue or sometimes in hollow organs such as the bladder or uterus. RMS can occur at any age, but it most often affects children. Rhabdomyosarcoma (RMS) can affect the head, neck, bladder, vagina, arms, legs, trunk, or just about any body part. Cells from rhabdomyosarcomas are often fast growing and can spread (metastasize) to other parts of the body. RMS is a very rare cancer. There are only about 350 cases of RMS diagnosed each year in the United States in children under the age of 21 years.

Types of Rhabdomyosarcoma (RMS) Tumors

Following are the two main types of Rhabdomyosarcoma (RMS) are:
  • Embryonal Rhabdomyosarcoma (ERMS): ERMS usually affects children in their first 5 years of life, but it can occur at older ages as well. ERMS tends to occur in the head and neck area, bladder, vagina, or in or around the prostate and testicles.

    Two subtypes of ERMS:
  • Botryoid Rhabdomyosarcoma
  • Spindle Cell Rhabdomyosarcomas, tend to have a better prognosis (outlook) than the more common conventional form of ERMS.
  • Alveolar Rhabdomyosarcoma (ARMS): ARMS typically affects all age groups equally. It makes up a larger portion of RMS in older children, teens, and adults than in younger children (because ERMS is less common at older ages). ARMS most often occurs in large muscles of the trunk, arms, and legs. ARMS tends to grow faster than ERMS, and it usually requires more intense treatment. However, in some cases of ARMS, the cancer cells lack certain gene changes, which makes these cancers act more like ERMS.

Causes of Rhabdomyosarcoma (RMS) Tumors

The cause of most cases of Rhabdomyosarcoma (RMS) are unknown, and there are very few known risk factors for this type of cancer. But researchers are learning how normal cells become cancerous because of certain changes in their DNA.

Some patients with Rhabdomyosarcoma (RMS) have inherited gene changes from a parent that put them at higher risk. For example, people with Li-Fraumeni syndrome have changes in the p53 tumor-suppressor gene, which cause it to make a defective p53 protein. The p53 protein normally causes cells with DNA damage to either pause and repair that damage or, if repair is not possible, to self-destruct. When p53 is not working, cells with DNA damage keep dividing, which can lead to further defects in other genes, and eventually causing cancer.

Gene changes in Alveolar Rhabdomyosarcoma (ARMS)

Certain genes in a cell can be turned on when bits of DNA are switched from one chromosome to another. This type of change, called a translocation, can happen when a cell is dividing into 2 new cells. This seems to be the cause of most cases of alveolar rhabdomyosarcoma (ARMS). In these cancers, a small piece of chromosome 2 (or, less often, chromosome 1) often ends up on chromosome 13. This moves a gene called PAX3 (or PAX7 if it’s chromosome 1) right next to a gene called FOXO1, creating a PAX/FOX01 fusion gene. The PAX genes play an important role in cell growth while an embryo’s muscle tissue is being formed, but these genes usually shut down once they’re no longer needed. Moving one of them next to the FOXO1 gene keeps the PAX gene active, which seems to be what leads to the tumor forming.

Other translocations or other types of gene changes are also sometimes seen in ARMS. In fact, about 1 out of 4 cancers that doctors would usually classify as ARMS have been found not to have the PAX/FOXO1 fusion gene typically seen in ARMS. Researchers have found that these cancers act more like embryonal rhabdomyosarcoma (ERMS), which generally requires less intensive treatment than ARMS.

Gene changes in Embryonal Rhabdomyosarcoma (ERMS)

Research suggests that embryonal rhabdomyosarcoma (ERMS) develops in a different way. Cells of this tumor typically have lost a small piece of chromosome 11 that came from a person’s mother, and it has been replaced by a second copy of that part of the chromosome from their father. This seems to make the IGF2 gene on chromosome 11 overactive. The IGF2 gene codes for a protein that can make these tumor cells grow. Other gene changes are probably important in these tumors as well.

Bay Biosciences is a global leader in providing researchers with high quality, clinical grade, fully characterized human tissue samples, bio-specimens and human bio-fluid collections from cancer (tumor) tissue, cancer serum, cancer plasma cancer PBMC and human tissue samples from most other therapeutic areas and diseases.

Bay Biosciences maintains and manages it’s own bio-repository, human tissue bank (biobank) consisting of thousands of diseased samples (specimens) and from normal healthy donors available in all formats and types. Our biobank procures and stores fully consented, deidentified and institutional review boards (IRB) approved human tissue samples and matched controls.

All our human human tissue collections, human specimens and human bio-fluids are provided with detailed samples associated patient’s clinical data. This critical patient’s clinical data includes information relating to their past and current disease, treatment history, lifestyle choices, biomarkers and genetic information. Patient’s data is extremely valuable for researchers and is used to help identify new effective treatments (drug discovery & development) in oncology, other therapeutic areas and diseases. This clinical information is critical to demonstrate their impact, monitor the safety of medicines, testing & diagnostics, and generate new knowledge about the causes of disease and illness. 

Bay Biosciences banks wide variety of human tissue samples and biological samples including cryogenically preserved -80°C, fresh, fresh frozen tissue samplestumor tissue samples, FFPE’s, tissue slides, with matching human bio-fluids, whole blood and blood derived products such as serumplasma and PBMC’s.

Bay Biosciences is a global leader in collecting and providing human tissue samples according to the researchers specified requirements and customized, tailor made collection protocols. Please contact us anytime to discuss your special research projects and customized human tissue sample requirements.

Bay Biosciences provides human tissue samples (human specimens) from diseased and normal healthy donors; including peripheral whole-blood, amniotic fluid, bronchoalveolar lavage fluid (BAL), sputum, pleural effusion, cerebrospinal fluid (CSF), serum (sera), plasma, peripheral blood mononuclear cells (PBMC’s), saliva, Buffy coat, urine, stool samples, aqueous humor, vitreous humor, kidney stones, renal calculi, nephrolithiasis, urolithiasis and other bodily fluids from most diseases including cancer. We can also procure most human bio-specimens and can do special collections and requests of human samples that are difficult to find. All our human tissue samples are procured through IRB approved clinical protocols and procedures. 

In addition to the standard processing protocols Bay Biosciences can also provide human plasma, serum, PBMC bio-fluid samples using custom processing protocols, you can buy donor specific sample collections in higher volumes and specified sample aliquoting from us. Bay Biosciences also provides human samples from normal healthy donors, volunteers, for controls and clinical research, contact us Now.

 

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